
Cardiomyopathy, hypertrophic. Oblique axial cine magnetic resonance angiogram in the same patient as in Image above shows a spade-shaped left ventricle with relative sparing of the apical myocardium (arrow)
A disease of the myocardium (the muscle of the heart) in which a portion of the myocardium is hypertrophied (thickened). hypertrophic cardiomyopathy is a significant cause of sudden unexpected cardiac death in any age group
I Genetics
Hypertrophic cardiomyopathy is inherited as an autosomal dominant trait
The incidence of HCM is about 0.2% to 0.5% of the general population
Obstructive and non-obstructive
Depending on whether the distortion of normal heart anatomy causes an obstruction of the outflow of blood from the left ventricle of the heart, HCM can be defined as obstructive or non-obstructive.
II Associated symptoms
dyspnea (shortness of breath), chest pain (sometimes known as angina), uncomfortable awareness of the heart beat (palpitations), lightheadedness, fatigue, fainting (called syncope) and sudden cardiac death
III Diagnostic testing
echocardiography, cardiac catheterization, cardiac MRI in the diagnosis of the disease, other important factors include ECG and genetic test .
IV Treatment
Medicine:
The first medication that is routinely used is a beta-blocker, calcium channel blocker such as verapamil may be substituted for a beta block
If symptoms and gradient persist, disopyramide (Class Ia antiarrhythmic (sodium channel blocker))
may be added to the beta-blocker.
to relieve symptoms in patients who remain severely symptomatic despite medical therapy
Surgical myectomy
Alcohol septal ablation
Ventricular pacing
Plz read more MSCT or MRI?
Diagnosis of Coronary Stenosis with CT Angiography (09/02/2011) tachycardia (09/02/2011) Calcium Boosts Heart Attack Risk (10/01/2011) Acute Pericarditis (25/12/2010) RESTRICTIVE CARDIOMYOPATHY (25/12/2010) Swan-Ganz catheterization (25/12/2010) Tricuspid Regurgitation (25/12/2010) Tricuspid stenosis (25/12/2010) Aortic regurgitation (25/12/2010) Aortic Stenosis (25/12/2010)